CFDB - Cystic Fibrosis DataBase

primary studies published RCT

Effect of hypertonic saline, amiloride, and cough on mucociliary clearance in patients with cystic fibrosis.

Study design (if review, criteria of inclusion for studies)

Randomised cross-over trial

Participants

Mean age 16.5 years, range 13 years to 20 years n = 10 Males = 3, females = 7 Participants were recruited as they were admitted with exacerbations of their lung disease with cough productive of tenacious sputum Severity of lung disease; median FEV1 as % predicted 72, median FVC % predicted 53.5

Interventions

Cross-over to IS daily for 2 days (control group) Pre-treated with nebulised salbutamol 5 mg HS 6% daily for 2 days (treatment group)

Outcome measures

Sputum weight VAS, feeling of cleared chest

Main results

The percent cleared at 60 and 90 min was significantly increased with HS (%C60 = 26.5%, %C90 = 29.4%) and the combination of AML + HS (%C60 = 23.1%, %C90 = 27.4%) compared with both IS (%C60 = 14.7%, %C90 = 17.5%) and COUGH (%C60 = 18.0%, %C90 = 19.5%), p < 0.01. Inhalation of hypertonic saline is a potentially useful treatment in patients with cystic fibrosis.

Keywords: Amiloride; hydration; Hypertonic Solutions; pharmacological_intervention; Airway clearance drugs -expectorants- mucolytic- mucociliary-; ENaC antagonists - Sodium Channel Blockers; Respiratory System Agents;