CFDB - Cystic Fibrosis DataBase

primary studies published RCT

Effects of glutamine and recombinant human growth hormone on protein metabolism in prepubertal children with cystic fibrosis.

Study design (if review, criteria of inclusion for studies)

RCT

Participants

9 (9.6 +/- 0.5-yr-old) children with CF who were either undernourished (weight/height, <50th percentile) or short (height, <5th percentile)

Interventions

patients received 2-h infusions of [(13)C]bicarbonate (to assess CO(2) production), followed by 4-h infusions of [(13)C]leucine and [(15)N]GLN, on 4 separate days in the postabsorptive state: 1) at baseline, and after a 4-wk treatment with 2) oral GLN (0.7 g/kg.d), 3) rhGH (0.3 mg/kg.wk), and 4) GLN and rhGH combined (GLN and rhGH regimens were in randomized order).

Outcome measures

leucine kinetics, leucine oxidation, proteolysis or GLN kinetics

Main results

No significant effect of GLN on leucine kinetics was detectable. In contrast, rhGH induced a 32% reduction in leucine oxidation and a 13% stimulation of nonoxidative leucine disposal, an index of protein synthesis (P < 0.05), with no change in proteolysis or GLN kinetics. The combined GLN plus rhGH regimen had similar effects as rhGH alone.

Authors' conclusions

In children with CF, 1) oral GLN may not promote protein gain in the fasting state; and 2) a short course of rhGH has a potent anabolic effect that is mediated by stimulation of protein synthesis and does not affect GLN kinetics.

Keywords: Amino Acids; Child; Glutamine; Growth Hormone; Hormones; Malnutrition; non pharmacological intervention - diet; Nutrition Disorders; pharmacological_intervention; Proteins; Recombinant Proteins; Supplementation; Combined Modality Therapy; Oral; rhGH;