CFDB - Cystic Fibrosis DataBase

primary studies published, non RCT

Lung Clearance Index and Structural Lung Disease on Computed Tomography in Early Cystic Fibrosis.

Study design (if review, criteria of inclusion for studies)

observational diagnostic study

Participants

42 infants (ages 0-2 yr), 39 preschool children (ages 3-6 yr), and 38 school-age children (7-16 yr) with CF and 72 healthy control subjects.

Interventions

Lung clearance index was assessed before chest computed tomography.

Outcome measures

Scans were evaluated for CF-related structural lung disease using the Perth-Rotterdam Annotated Grid Morphometric Analysis for Cystic Fibrosis quantitative outcome measure.

Main results

In infants with CF, lung clearance index is insensitive to structural disease (kappa = -0.03 [95% confidence interval, -0.05 to 0.16]). In preschool children with CF, lung clearance index correlates with total disease extent. In school-age children, lung clearance index correlates with extent of total disease, bronchiectasis, and air trapping. In preschool and school-age children, lung clearance index has a good positive predictive value (83-86%) but a poor negative predictive value (50-55%) to detect the presence of bronchiectasis.

Authors' conclusions

These data suggest that lung clearance index may be a useful surveillance tool to monitor structural lung disease in preschool and school-age children with CF. However, lung clearance index cannot replace chest computed tomography to screen for bronchiectasis in this population.

Keywords: Child; computed tomography; non pharmacological intervention - diagn; diagnostic procedures; Lung Clearance Index;