CFDB - Cystic Fibrosis DataBase

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KB001-A, a novel anti-inflammatory, found to be safe and well-tolerated in cystic fibrosis patients infected with Pseudomonas aeruginosa.

primary studies  published RCT

Details
  • 2018
  • Jain R

Antibiotic exposure and interpersonal variance mask the effect of ivacaftor on respiratory microbiota composition.

primary studies  published RCT

Details
  • 2018
  • Peleg AY

Study design considerations for the Standardized Treatment of Pulmonary Exacerbations 2 (STOP2): A trial to compare intravenous antibiotic treatment durations in CF.

primary studies  published RCT

Details
  • 2018
  • Heltshe SL

Children and Adults Tai Chi Study (CF-CATS2): a randomised controlled feasibility study comparing internet-delivered with face-to-face Tai Chi lessons in cystic fibrosis.

primary studies  published RCT

Details
  • 2018
  • Carr SB

Influence of the Vibralung Acoustical Percussor on pulmonary function and sputum expectoration in individuals with cystic fibrosis.

primary studies  published RCT

Details
  • 2018
  • Wheatley CM

Preventative Inhalation of Hypertonic Saline in Infants with Cystic Fibrosis (PRESIS): A Randomized, Double-Blind, Controlled Study.

primary studies  published RCT

Details
  • 2018
  • Stahl M

Effectiveness of a Home-Based Active Video Game Programme in Young Cystic Fibrosis Patients.

primary studies  published RCT

Details
  • 2018
  • Del Corral T

The role of small intestinal bacterial overgrowth in cystic fibrosis: a randomized case-controlled clinical trial with rifaximin.

primary studies  published RCT

Details
  • 2018
  • Furnari M

VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

primary studies  published RCT

Details
  • 2018
  • Keating D

Probiotics in cystic fibrosis patients: a double blind crossover placebo controlled study: pilot study from the ESPGHAN Working Group on Pancreas/CF

primary studies  published RCT

Details
  • 2018
  • Van Biervliet S