CFDB - Cystic Fibrosis DataBase

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All subcategories » published, non RCT

Non-invasive evaluation of steatosis and fibrosis in the liver in adults patients living with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2025
  • Piñar-Gutiérrez A

Respiratory Outcomes and Aspergillus Serology Following Elexacaftor/Tezacaftor/Ivacaftor Therapy in People with Cystic Fibrosis and a History of Aspergillus fumigatus Infection.

primary studies  published, non RCT

Details
  • 2025
  • Lanfranchi C

Point of care lung ultrasound in preschool children with cystic fibrosis: a case-controlled, prospective, pilot study.

primary studies  published, non RCT

Details
  • 2024
  • Crispino AA

Successful Therapy over 12 Months of People with Cystic Fibrosis with Rare Non-phe508del Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Mutations with Elexacaftor/Tezacaftor/Ivacaftor (ETI).

primary studies  published, non RCT

Details
  • 2024
  • Sütering T

Long-term therapy with CFTR modulators consistently improves glucose metabolism in adolescents and adults with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2024
  • Cohen A

The long-term effect of elexacaftor/tezacaftor/ivacaftor on cardiorespiratory fitness in adolescent patients with cystic fibrosis: a pilot observational study.

primary studies  published, non RCT

Details
  • 2024
  • Stastna N

Long-term outcomes of early exposure to repeated general anaesthesia in children with cystic fibrosis (CF-GAIN): a multicentre, open-label, randomised controlled phase 4 trial.

primary studies  published, non RCT

Details
  • 2024
  • Wainwright CE

Airway clearance therapy in the school environment: Retrospective analysis of a cohort of pediatric patients with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2023
  • Byrwa DJ

Echocardiographic assessment of cardiovascular involvements in children with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2024
  • Ghaffaripour H

Impact of chronic medication de-escalation in patients with cystic fibrosis taking elexacaftor, tezacaftor, ivacaftor: A retrospective review.

primary studies  published, non RCT

Details
  • 2024
  • Guenther EL