CFDB - Cystic Fibrosis DataBase

at least one term
all terms

Cannabinoid receptor 2 agonist, lenabasum, for the treatment of pulmonary exacerbations in cystic fibrosis.

primary studies  published RCT

Details
  • 2025
  • West NE

MetaNeb Versus Usual Care During Exacerbations of Cystic Fibrosis: An RCT.

primary studies  published RCT

Details
  • 2025
  • Chapman N

Randomized Cross-Over Analysis of the Influence of Nitrogen Multiple Breath Washout on Spirometry in Monitoring Lung Function in Patients With Cystic Fibrosis and Primary Ciliary Dyskinesia.

primary studies  published RCT

Details
  • 2025
  • Schoop AC

Cystic Fibrosis Microbiome-directed Antibiotic Therapy Trial in Exacerbations Results Stratified (CFMATTERS): Results of a multi-centre randomised controlled trial.

primary studies  published RCT

Details
  • 2025
  • Plant BJ

The impact of probiotics on pulmonary, gastrointestinal, and growth outcomes in pediatric cystic fibrosis: a randomized controlled trial.

primary studies  published RCT

Details
  • 2025
  • Rahmani P

Insulin for early glycaemic abnormality in children with cystic fibrosis without cystic fibrosis-related diabetes (CF-IDEA): a randomised controlled trial.

primary studies  published RCT

Details
  • 2025
  • Hameed S

Elexacaftor/tezacaftor/ivacaftor in children aged ≥6 years with cystic fibrosis heterozygous for F508del and a minimal function mutation: Results from a 96-week open-label extension study.

primary studies  published RCT

Details
  • 2025
  • Mall MA

The Effects of Progressive Muscle Relaxation on Mental Health and Sleep Quality in Adults with Cystic Fibrosis: A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2025
  • Maritescu A

Effects of Oral Amino Acid Supplementation on Physical Activity, Systemic Inflammation, and Quality of Life in Adult Patients with Cystic Fibrosis: A Single-Center, Randomized, Double-Blind, Placebo-Controlled Pilot Study.

primary studies  published RCT

Details
  • 2025
  • Petraglia L

Vanzacaftor-tezacaftor-deutivacaftor versus elexacaftor-tezacaftor-ivacaftor in individuals with cystic fibrosis aged 12 years and older (SKYLINE Trials VX20-121-102 and VX20-121-103): results from two randomised, active-controlled, phase 3 trials.

primary studies  published RCT

Details
  • 2024
  • Keating C