CFDB - Cystic Fibrosis DataBase

at least one term
all terms

Small airway deposition of dornase alfa during exacerbations in cystic fibrosis; A randomized controlled clinical trial.

primary studies  published RCT

Details
  • 2014
  • Bakker EM

Open randomised prospective comparative multi-centre intervention study of patients with cystic fibrosis and early diagnosed diabetes mellitus.

primary studies  published RCT

Details
  • 2014
  • Ballmann M

Fat-soluble vitamins in cystic fibrosis and pancreatic insufficiency: Efficacy of a nutrition intervention.

primary studies  published RCT

Details
  • 2014
  • Bertolaso C

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial.

primary studies  published RCT

Details
  • 2014
  • Boyle MP

Testing Two Different Doses of Tiotropium Respimat(R) in Cystic Fibrosis: Phase 2 Randomized Trial Results.

primary studies  published RCT

Details
  • 2014
  • Bradley JM

Disrupted intestinal microbiota and intestinal inflammation in children with cystic fibrosis and its restoration with Lactobacillus GG: a randomised clinical trial.

primary studies  published RCT

Details
  • 2014
  • Bruzzese E

Randomized, single blind, controlled trial of inhaled glutathione vs placebo in patients with cystic fibrosis

primary studies  published RCT

Details
  • 2014
  • Calabrese C

Long-term treatment with oral N-acetylcysteine: Affects lung function but not sputum inflammation in cystic fibrosis subjects. A phase II randomized placebo-controlled trial.

primary studies  published RCT

Details
  • 2014
  • Conrad C

Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation

primary studies  published RCT

Details
  • 2014
  • De Boeck K

Improvement of digestive health and reduction in proteobacterial populations in the gut microbiota of cystic fibrosis patients using a Lactobacillus reuteri probiotic preparation: a double blind prospective study.

primary studies  published RCT

Details
  • 2014
  • del Campo R