CFDB - Cystic Fibrosis DataBase

at least one term
all terms

Benefits of neuromuscular electrical stimulation prior to endurance training in patients with cystic fibrosis and severe pulmonary dysfunction.

primary studies  published RCT

Details
  • 2013
  • Vivodtzev I

Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study.

primary studies  published RCT

Details
  • 2012
  • Aaron SD

CPAP has no effect on clearance, sputum properties, or expectorated volume in cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Aquino ES

Liprotamase long-term safety and support of nutritional status in pancreatic-insufficient cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Borowitz D

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.

primary studies  published RCT

Details
  • 2012
  • Clancy JP

Adults with cystic fibrosis prefer hypertonic saline before or during airway clearance techniques: a randomised crossover trial.

primary studies  published RCT

Details
  • 2012
  • Dentice RL

Efficacy, safety and effect on biomarkers of AZD9668 in cystic fibrosis

primary studies  published RCT

Details
  • 2012
  • Elborn JS

A randomized, double-blind, placebo-controlled trial of cyproheptadine for appetite stimulation in cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Epifanio M

Ivacaftor in subjects with cystic fibrosis who are homozygous for the F508del-CFTR mutation.

primary studies  published RCT

Details
  • 2012
  • Flume PA

Nebulized hypertonic saline containing hyaluronic acid improves tolerability in patients with cystic fibrosis and lung disease compared with nebulized hypertonic saline alone: a prospective, randomized, double-blind, controlled study.

primary studies  published RCT

Details
  • 2012
  • Furnari ML