CFDB - Cystic Fibrosis DataBase

at least one term
all terms

Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate.

primary studies  published RCT

Details
  • 2002
  • Zeitlin PL

Effect of insulinlike growth factor-1 treatment in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Bucuvalas JC

Cystic fibrosis-related deaths in infancy and the effect of newborn screening.

primary studies  published RCT

Details
  • 2001
  • Doull IJ

RAD in stable lung and heart/lung transplant recipients: safety, tolerability, pharmacokinetics, and impact of cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Doyle RL

Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group.

primary studies  published RCT

Details
  • 2001
  • Farrell PM

In vivo physiologic comparison of two ventilators used for domiciliary ventilation in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Fauroux B

Growth hormone improves clinical status in prepubertal children with cystic fibrosis: results of a randomized controlled trial.

primary studies  published RCT

Details
  • 2001
  • Hardin DS

Growth hormone decreases protein catabolism in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Hardin DS

Effect of intravenous pamidronate on bone mineral density in adults with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Haworth CS

Glucocorticoid treatment reduces exhaled nitric oxide in cystic fibrosis patients.

primary studies  published RCT

Details
  • 2001
  • Linnane SJ