CFDB - Cystic Fibrosis DataBase

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Impact of pharmacy services on time to elexacaftor-tezacaftor-ivacaftor initiation.

primary studies  published RCT

Details
  • 2022
  • Roder L

Feasibility and efficacy of combined pancreatic islet-lung transplantation in cystic fibrosis related diabetes -PIM study: a multicenter phase 1-2 trial.

primary studies  published RCT

Details
  • 2022
  • Rakotoarisoa L

The Effect of Control IQ Hybrid Closed Loop Technology on Glycemic Control in Adolescents and Adults with Cystic Fibrosis-Related Diabetes.

primary studies  published RCT

Details
  • 2022
  • Scully KJ

The Short Term Influence of Chest Physiotherapy on Lung Function Parameters in Children With Cystic Fibrosis and Primary Ciliary Dyskinesia.

primary studies  published RCT

Details
  • 2022
  • Vandervoort B

The Role of Bronchoscopy in the Management of Children With Cystic Fibrosis.

primary studies  published RCT

Details
  • 2022
  • Tosco A

Maternal and fetal outcomes following elexacaftor-tezacaftor-ivacaftor use during pregnancy and lactation.

primary studies  published RCT

Details
  • 2021
  • Taylor-Cousar JL

Lumacaftor/ivacaftor in cystic fibrosis: effects on glucose metabolism and insulin secretion.

primary studies  published RCT

Details
  • 2021
  • Colombo C

Clinical Effectiveness of Elexacaftor/Tezacftor/Ivacaftor in People with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2021
  • Nichols DP

The long-term safety of chronic azithromycin use in adult patients with cystic fibrosis, evaluating biomarkers for renal function, hepatic function and electrical properties of the heart.

primary studies  published RCT

Details
  • 2021
  • Akkerman-Nijland AM

Change in Nutrient and Dietary Intake in European Children with Cystic Fibrosis after a 6-Month Intervention with a Self-Management mHealth Tool.

primary studies  published RCT

Details
  • 2021
  • Calvo-Lerma J