CFDB - Cystic Fibrosis DataBase

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Evidence for safety and efficacy of DOTAP cationic liposome mediated CFTR gene transfer to the nasal epithelium of patients with cystic fibrosis.

primary studies  published RCT

Details
  • 1997
  • Porteous DJ

Oral ciprofloxacin vs. intravenous ceftazidime plus tobramycin in pediatric cystic fibrosis patients: comparison of antipseudomonas efficacy and assessment of safety with ultrasonography and magnetic resonance imaging. Cystic Fibrosis Study Group.

primary studies  published RCT

Details
  • 1997
  • Richard DA

Effect of increasing doses of hypertonic saline on mucociliary clearance in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 1997
  • Robinson M

Ciprofloxacin as antipseudomonal treatment in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 1997
  • Schaad UB

Effect of supplemental oxygen on supramaximal exercise performance and recovery in cystic fibrosis.

primary studies  published RCT

Details
  • 1997
  • Shah AR

An evaluation of two aerosol delivery systems for rhDNase.

primary studies  published RCT

Details
  • 1997
  • Shah PL

Lower respiratory illness in infants and young children with cystic fibrosis: evaluation of treatment with intravenous hydrocortisone.

primary studies  published RCT

Details
  • 1997
  • Tepper RS

Low-dose versus high-dose ursodeoxycholic acid in cystic fibrosis-related cholestatic liver disease. Results of a randomized study with 1-year follow-up.

primary studies  published RCT

Details
  • 1997
  • van de Meeberg PC

Comparison of DNA-lipid complexes and DNA alone for gene transfer to cystic fibrosis airway epithelia in vivo.

primary studies  published RCT

Details
  • 1997
  • Zabner J

Ursodeoxycholic acid for liver disease associated with cystic fibrosis: a double-blind multicenter trial. The Italian Group for the Study of Ursodeoxycholic Acid in Cystic Fibrosis.

primary studies  published RCT

Details
  • 1996
  • Colombo C