CFDB - Cystic Fibrosis DataBase

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Safety and Efficacy of a Novel Microbial Lipase in Patients with Exocrine Pancreatic Insufficiency due to Cystic Fibrosis: A Randomized Controlled Clinical Trial.

primary studies  published RCT

Details
  • 2016
  • Heubi JE

Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study.

primary studies  published RCT

Details
  • 2016
  • Konstan MW

One-year safety and efficacy of tobramycin powder for inhalation in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2016
  • Konstan MW

Short-Term Effect of Different Physical Exercises and Physiotherapy Combinations on Sputum Expectoration, Oxygen Saturation, and Lung Function in Young Patients with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2016
  • Kriemler S

Sino nasal inhalation of isotonic versus hypertonic saline (6.0%) in CF patients with chronic rhinosinusitis - Results of a multicenter, prospective, randomized, double-blind, controlled trial.

primary studies  published RCT

Details
  • 2016
  • Mainz JG

Clinical impact of vitamin D treatment in cystic fibrosis: a pilot randomized, controlled trial.

primary studies  published RCT

Details
  • 2016
  • Pincikova T

Non-invasive Ventilation as Airway Clearance Technique in Cystic Fibrosis.

primary studies  published RCT

Details
  • 2016
  • Rodriguez Hortal MC

A randomized controlled trial of vitamin D replacement strategies in pediatric CF patients.

primary studies  published RCT

Details
  • 2016
  • Simoneau T

Effect of Oral Lipid Matrix Supplement on Fat Absorption in Cystic Fibrosis: A Randomized Placebo-Controlled Trial.

primary studies  published RCT

Details
  • 2016
  • Stallings VA

Comparison of two pancreatic enzyme products for exocrine insufficiency in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2016
  • Taylor CJ