CFDB - Cystic Fibrosis DataBase

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Repeated nebulisation of non-viral CFTR gene therapy in patients with cystic fibrosis: a randomised, double-blind, placebo-controlled, phase 2b trial.

primary studies  published RCT

Details
  • 2015
  • Alton EW

A possible alternative exercise test for youths with cystic fibrosis: the steep ramp test.

primary studies  published RCT

Details
  • 2015
  • Bongers BC

Use of ibuprofen to assess inflammatory biomarkers in induced sputum: Implications for clinical trials in cystic fibrosis.

primary studies  published RCT

Details
  • 2015
  • Chmiel JF

Ciprofloxacin during upper respiratory tract infections to reduce Pseudomonas aeruginosa infection in paediatric cystic fibrosis: a pilot study.

primary studies  published RCT

Details
  • 2015
  • Connett GJ

Ciprofloxacin DPI: a randomised, placebo-controlled, phase IIb efficacy and safety study on cystic fibrosis.

primary studies  published RCT

Details
  • 2015
  • Dorkin HL

Non-invasive ventilation used as an adjunct to airway clearance treatments improves lung function during an acute exacerbation of cystic fibrosis: a randomised trial.

primary studies  published RCT

Details
  • 2015
  • Dwyer TJ

A phase 3, open-label, randomized trial to evaluate the safety and efficacy of levofloxacin inhalation solution (APT-1026) versus tobramycin inhalation solution in stable cystic fibrosis patients

primary studies  published RCT

Details
  • 2015
  • Elborn JS

Glutamine supplementation in cystic fibrosis: A randomized placebo-controlled trial.

primary studies  published RCT

Details
  • 2015
  • Forrester DL

Efficacy response in CF patients treated with ivacaftor: Post-hoc analysis.

primary studies  published RCT

Details
  • 2015
  • Konstan MW

Efficacy and safety of ivacaftor in patients with cystic fibrosis who have an Arg117His-CFTR mutation: a double-blind, randomised controlled trial.

primary studies  published RCT

Details
  • 2015
  • Moss RB