CFDB - Cystic Fibrosis DataBase

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Oral Reduced L-Glutathione Improves Growth in Pediatric Cystic Fibrosis Patients: A Randomized Clinical Trial.

primary studies  published RCT

Details
  • 2015
  • Visca A

Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.

primary studies  published RCT

Details
  • 2015
  • Wainwright CE

Moderate intensity exercise mediates comparable increases in exhaled chloride as albuterol in individuals with cystic fibrosis.

primary studies  published RCT

Details
  • 2015
  • Wheatley CM

Randomized controlled trial of biofilm antimicrobial susceptibility testing in cystic fibrosis patients.

primary studies  published RCT

Details
  • 2015
  • Yau YC

Sweat chloride as a biomarker of CFTR activity: Proof of concept and ivacaftor clinical trial data.

primary studies  published RCT

Details
  • 2014
  • Accurso FJ

Nebulized tobramycin in the treatment of adult cf pulmonary exacerbations.

primary studies  published RCT

Details
  • 2014
  • Al-Aloul M

Small airway deposition of dornase alfa during exacerbations in cystic fibrosis; A randomized controlled clinical trial.

primary studies  published RCT

Details
  • 2014
  • Bakker EM

Open randomised prospective comparative multi-centre intervention study of patients with cystic fibrosis and early diagnosed diabetes mellitus.

primary studies  published RCT

Details
  • 2014
  • Ballmann M

Fat-soluble vitamins in cystic fibrosis and pancreatic insufficiency: Efficacy of a nutrition intervention.

primary studies  published RCT

Details
  • 2014
  • Bertolaso C

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial.

primary studies  published RCT

Details
  • 2014
  • Boyle MP