CFDB - Cystic Fibrosis DataBase

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Benefits of combining inspiratory muscle with 'whole muscle' training in children with cystic fibrosis: a randomised controlled trial.

primary studies  published RCT

Details
  • 2013
  • Santana-Sosa E

Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in patients with cystic fibrosis: a randomised study.

primary studies  published RCT

Details
  • 2013
  • Schuster A

Inhaled aztreonam for chronic Burkholderia infection in cystic fibrosis: A placebo-controlled trial.

primary studies  published RCT

Details
  • 2013
  • Tullis DE

Benefits of neuromuscular electrical stimulation prior to endurance training in patients with cystic fibrosis and severe pulmonary dysfunction.

primary studies  published RCT

Details
  • 2013
  • Vivodtzev I

Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study.

primary studies  published RCT

Details
  • 2012
  • Aaron SD

CPAP has no effect on clearance, sputum properties, or expectorated volume in cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Aquino ES

Liprotamase long-term safety and support of nutritional status in pancreatic-insufficient cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Borowitz D

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.

primary studies  published RCT

Details
  • 2012
  • Clancy JP

Adults with cystic fibrosis prefer hypertonic saline before or during airway clearance techniques: a randomised crossover trial.

primary studies  published RCT

Details
  • 2012
  • Dentice RL

Efficacy, safety and effect on biomarkers of AZD9668 in cystic fibrosis

primary studies  published RCT

Details
  • 2012
  • Elborn JS