CFDB - Cystic Fibrosis DataBase

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A randomized, double-blind, placebo-controlled trial of cyproheptadine for appetite stimulation in cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Epifanio M

Ivacaftor in subjects with cystic fibrosis who are homozygous for the F508del-CFTR mutation.

primary studies  published RCT

Details
  • 2012
  • Flume PA

Nebulized hypertonic saline containing hyaluronic acid improves tolerability in patients with cystic fibrosis and lung disease compared with nebulized hypertonic saline alone: a prospective, randomized, double-blind, controlled study.

primary studies  published RCT

Details
  • 2012
  • Furnari ML

Oral magnesium supplementation in children with cystic fibrosis improves clinical and functional variables: a double-blind, randomized, placebo-controlled crossover trial.

primary studies  published RCT

Details
  • 2012
  • Gontijo-Amaral C

Pilot study of vitamin D supplementation in adults with cystic fibrosis pulmonary exacerbation: A randomized, controlled trial.

primary studies  published RCT

Details
  • 2012
  • Grossmann RE

Impact of vitamin D supplementation on markers of inflammation in adults with cystic fibrosis hospitalized for a pulmonary exacerbation.

primary studies  published RCT

Details
  • 2012
  • Grossmann RE

Comparison of effects of 3 and 7% hypertonic saline nebulization on lung function in children with cystic fibrosis: a double-blind randomized, controlled trial.

primary studies  published RCT

Details
  • 2012
  • Gupta S

A randomized placebo-controlled trial of miglustat in cystic fibrosis based on nasal potential difference.

primary studies  published RCT

Details
  • 2012
  • Leonard A

Long term effects of denufosol tetrasodium in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Ratjen F

Effect of azithromycin on systemic markers of inflammation in cystic fibrosis patients uninfected with Pseudomonas aeruginosa.

primary studies  published RCT

Details
  • 2012
  • Ratjen F