CFDB - Cystic Fibrosis DataBase

at least one term
all terms

A four week trial of hypertonic saline in children with mild cystic fibrosis lung disease: Effect on mucociliary clearance and clinical outcomes.

primary studies  published RCT

Details
  • 2020
  • Donaldson SH

Aerosolized lancovutide in adolescents (≥12 years) and adults with cystic fibrosis - a randomized trial.

primary studies  published RCT

Details
  • 2020
  • Eber E

Improved residual fat malabsorption and growth in children with cystic fibrosis treated with a novel oral structured lipid supplement: A randomized controlled trial.

primary studies  published RCT

Details
  • 2020
  • Stallings VA

Correction: Improved residual fat malabsorption and growth in children with cystic fibrosis treated with a novel oral structured lipid supplement: A randomized controlled trial.

primary studies  published RCT

Details
  • 2020
  • Stallings VA

Effects of low glycemic index/high-fat, high-calorie diet on glycemic control and lipid profiles of children and adolescence with cystic fibrosis: A randomized double-blind controlled clinical trial.

primary studies  published RCT

Details
  • 2020
  • Gorji Z

Effects of synbiotic supplementation on the pulmonary manifestations and anthropometric measurements in children with cystic fibrosis- a randomized clinical trial

primary studies  published RCT

Details
  • 2020
  • N Bilan, E Marefat, M Nouri-Vaskeh, L Nikniaz, Z Nikniaz

Efficacy and safety of ataluren in patients with nonsense-mutation cystic fibrosis not receiving chronic inhaled aminoglycosides: The international, randomized, double-blind, placebo-controlled Ataluren Confirmatory Trial in Cystic Fibrosis (ACT CF).

primary studies  published RCT

Details
  • 2020
  • Konstan MW

A randomised controlled trial of rosuvastatin for the prevention of aminoglycoside-induced kidney toxicity in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2020
  • McWilliam SJ

CFTR activity is enhanced by the novel corrector GLPG2222, given with and without ivacaftor in two randomized trials.

primary studies  published RCT

Details
  • 2019
  • Bell SC

Non-invasive ventilation versus oxygen therapy in cystic fibrosis: A 12-month randomized trial.

primary studies  published RCT

Details
  • 2019
  • Milross MA