CFDB - Cystic Fibrosis DataBase

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Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial

primary studies  published RCT

Details
  • 2013
  • Davies J

Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with a G551D Mutation.

primary studies  published RCT

Details
  • 2013
  • Davies JC

Randomised Clinical Trial: Lactobacillus Reuteri ATCC55730 in Cystic Fibrosis.

primary studies  published RCT

Details
  • 2013
  • Di Nardo G

Dietary essential amino acids are highly anabolic in pediatric patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2013
  • Engelen MP

The effect of probiotics on fecal calprotectin in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2013
  • Fallahi G

Tobramycin inhalation powder manufactured by improved process in cystic fibrosis: the randomized EDIT trial.

primary studies  published RCT

Details
  • 2013
  • Galeva I

Iron supplementation does not worsen respiratory health or alter the sputum microbiome in cystic fibrosis.

primary studies  published RCT

Details
  • 2013
  • Gifford AH

A randomized controlled trial of inhaled l-Arginine in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2013
  • Grasemann H

Inhalation Treatment with Glutathione in Patients with Cystic Fibrosis: a Randomized Clinical Trial.

primary studies  published RCT

Details
  • 2013
  • Griese M

Effects of probiotics on quality of life in children with cystic fibrosis; a randomized controlled trial.

primary studies  published RCT

Details
  • 2013
  • Jafari SA