Liprotamase long-term safety and support of nutritional status in pancreatic-insufficient cystic fibrosis.
primary studies published RCT
Details- 2012
- Borowitz D
Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.
primary studies published RCT
Details- 2012
- Clancy JP
Adults with cystic fibrosis prefer hypertonic saline before or during airway clearance techniques: a randomised crossover trial.
primary studies published RCT
Details- 2012
- Dentice RL
Efficacy, safety and effect on biomarkers of AZD9668 in cystic fibrosis
primary studies published RCT
Details- 2012
- Elborn JS
A randomized, double-blind, placebo-controlled trial of cyproheptadine for appetite stimulation in cystic fibrosis.
primary studies published RCT
Details- 2012
- Epifanio M
Ivacaftor in subjects with cystic fibrosis who are homozygous for the F508del-CFTR mutation.
primary studies published RCT
Details- 2012
- Flume PA
Nebulized hypertonic saline containing hyaluronic acid improves tolerability in patients with cystic fibrosis and lung disease compared with nebulized hypertonic saline alone: a prospective, randomized, double-blind, controlled study.
primary studies published RCT
Details- 2012
- Furnari ML
Oral magnesium supplementation in children with cystic fibrosis improves clinical and functional variables: a double-blind, randomized, placebo-controlled crossover trial.
primary studies published RCT
Details- 2012
- Gontijo-Amaral C
Pilot study of vitamin D supplementation in adults with cystic fibrosis pulmonary exacerbation: A randomized, controlled trial.
primary studies published RCT
Details- 2012
- Grossmann RE
Impact of vitamin D supplementation on markers of inflammation in adults with cystic fibrosis hospitalized for a pulmonary exacerbation.
primary studies published RCT
Details- 2012
- Grossmann RE