CFDB - Cystic Fibrosis DataBase

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Comparison of effects of 3 and 7% hypertonic saline nebulization on lung function in children with cystic fibrosis: a double-blind randomized, controlled trial.

primary studies  published RCT

Details
  • 2012
  • Gupta S

A randomized placebo-controlled trial of miglustat in cystic fibrosis based on nasal potential difference.

primary studies  published RCT

Details
  • 2012
  • Leonard A

Long term effects of denufosol tetrasodium in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2012
  • Ratjen F

Effect of azithromycin on systemic markers of inflammation in cystic fibrosis patients uninfected with Pseudomonas aeruginosa.

primary studies  published RCT

Details
  • 2012
  • Ratjen F

Exercise with incorporated expiratory manoeuvres was as effective as breathing techniques for airway clearance in children with cystic fibrosis: a randomised crossover trial.

primary studies  published RCT

Details
  • 2012
  • Reix P

Clarithromycin therapy for patients with cystic fibrosis: a randomized controlled trial.

primary studies  published RCT

Details
  • 2012
  • Robinson P

Inhaled Hypertonic Saline in Infants and Children Younger Than 6 Years With Cystic Fibrosis: The ISIS Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2012
  • Rosenfeld M

Open-label, follow-on study of azithromycin in pediatric patients with CF uninfected with Pseudomonas aeruginosa.

primary studies  published RCT

Details
  • 2012
  • Saiman L

Intrahospital weight and aerobic training in children with cystic fibrosis: a randomized controlled trial.

primary studies  published RCT

Details
  • 2012
  • Santana Sosa E

Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in patients with cystic fibrosis: a randomised study.

primary studies  published RCT

Details
  • 2012
  • Schuster A