Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial.
primary studies published RCT
Details- 2021
- Spoletini G
Association of Intensity of Anti-Pseudomonal Antibiotic Therapy With Risk of Treatment-Emergent Organisms in Cystic Fibrosis Children with Newly Acquired Pseudomonas Aeruginosa.
primary studies published RCT
Details- 2021
- Cogen JD
Efficacy and safety of inhaled dry-powder mannitol in adults with cystic fibrosis: An international, randomized controlled study.
primary studies published RCT
Details- 2021
- Flume PA
Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial.
primary studies published RCT
Details- 2021
- Griese M
Reflex zone stimulation reduces ventilation inhomogeneity in cystic fibrosis: A randomised controlled cross-over study.
primary studies published RCT
Details- 2021
- Jana P
Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis.
primary studies published RCT
Details- 2021
- Voldby C
How Many Maneuvers Should We Do for Maximal Inspiratory and Expiratory Muscle Pressure Testing in Children: A Retrospective Review in Children with Cystic Fibrosis.
primary studies published RCT
Details- 2021
- Boonjindasup W
Empire-CF study: A phase 2 clinical trial of leukotriene A4 hydrolase inhibitor acebilustat in adult subjects with cystic fibrosis.
primary studies published RCT
Details- 2021
- Elborn JS
Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations.
primary studies published RCT
Details- 2020
- Munck A
Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study.
primary studies published RCT
Details- 2020
- Nick JA