CFDB - Cystic Fibrosis DataBase

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Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial.

primary studies  published RCT

Details
  • 2021
  • Spoletini G

Association of Intensity of Anti-Pseudomonal Antibiotic Therapy With Risk of Treatment-Emergent Organisms in Cystic Fibrosis Children with Newly Acquired Pseudomonas Aeruginosa.

primary studies  published RCT

Details
  • 2021
  • Cogen JD

Efficacy and safety of inhaled dry-powder mannitol in adults with cystic fibrosis: An international, randomized controlled study.

primary studies  published RCT

Details
  • 2021
  • Flume PA

Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial.

primary studies  published RCT

Details
  • 2021
  • Griese M

Reflex zone stimulation reduces ventilation inhomogeneity in cystic fibrosis: A randomised controlled cross-over study.

primary studies  published RCT

Details
  • 2021
  • Jana P

Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2021
  • Voldby C

How Many Maneuvers Should We Do for Maximal Inspiratory and Expiratory Muscle Pressure Testing in Children: A Retrospective Review in Children with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2021
  • Boonjindasup W

Empire-CF study: A phase 2 clinical trial of leukotriene A4 hydrolase inhibitor acebilustat in adult subjects with cystic fibrosis.

primary studies  published RCT

Details
  • 2021
  • Elborn JS

Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations.

primary studies  published RCT

Details
  • 2020
  • Munck A

Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study.

primary studies  published RCT

Details
  • 2020
  • Nick JA