CFDB - Cystic Fibrosis DataBase

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Triple Therapy for Cystic Fibrosis Phe508del-Gating and -Residual Function Genotypes.

primary studies  published RCT

Details
  • 2021
  • Barry PJ

Effects of a Partially Supervised Conditioning Program in Cystic Fibrosis: An International Multicenter Randomized Controlled Trial (ACTIVATE-CF).

primary studies  published RCT

Details
  • 2021
  • Hebestreit H

Interval versus constant-load exercise training in adults with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2021
  • Kaltsakas G

Effect of Sitagliptin on Islet Function in Pancreatic Insufficient Cystic Fibrosis With Abnormal Glucose Tolerance.

primary studies  published RCT

Details
  • 2021
  • Kelly A

Testing the effects of combining azithromycin with inhaled tobramycin for P. aeruginosa in cystic fibrosis: a randomised, controlled clinical trial.

primary studies  published RCT

Details
  • 2021
  • Nichols DP

Measurement properties of the one-minute sit-to-stand test in children and adolescents with cystic fibrosis: A multicenter randomized cross-over trial.

primary studies  published RCT

Details
  • 2021
  • Combret Y

A Randomized Trial of Antimicrobial Duration for Cystic Fibrosis Pulmonary Exacerbation Treatment.

primary studies  published RCT

Details
  • 2021
  • Goss CH

Amikacin liposome inhalation suspension for chronic Pseudomonas aeruginosa infection in cystic fibrosis.

primary studies  published RCT

Details
  • 2020
  • Bilton D

GLPG2737 in lumacaftor/ivacaftor-treated CF subjects homozygous for the F508del mutation: A randomized phase 2A trial (PELICAN).

primary studies  published RCT

Details
  • 2020
  • van Koningsbruggen-Rietschel S

Effect of Expiratory Muscle Training on Peak Cough Flow in Children and Adolescents with Cystic Fibrosis: A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2021
  • Emirza C