CFDB - Cystic Fibrosis DataBase

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Effect of Sitagliptin on Islet Function in Pancreatic Insufficient Cystic Fibrosis With Abnormal Glucose Tolerance.

primary studies  published RCT

Details
  • 2021
  • Kelly A

Testing the effects of combining azithromycin with inhaled tobramycin for P. aeruginosa in cystic fibrosis: a randomised, controlled clinical trial.

primary studies  published RCT

Details
  • 2021
  • Nichols DP

Measurement properties of the one-minute sit-to-stand test in children and adolescents with cystic fibrosis: A multicenter randomized cross-over trial.

primary studies  published RCT

Details
  • 2021
  • Combret Y

A Randomized Trial of Antimicrobial Duration for Cystic Fibrosis Pulmonary Exacerbation Treatment.

primary studies  published RCT

Details
  • 2021
  • Goss CH

Amikacin liposome inhalation suspension for chronic Pseudomonas aeruginosa infection in cystic fibrosis.

primary studies  published RCT

Details
  • 2020
  • Bilton D

GLPG2737 in lumacaftor/ivacaftor-treated CF subjects homozygous for the F508del mutation: A randomized phase 2A trial (PELICAN).

primary studies  published RCT

Details
  • 2020
  • van Koningsbruggen-Rietschel S

Effect of Expiratory Muscle Training on Peak Cough Flow in Children and Adolescents with Cystic Fibrosis: A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2021
  • Emirza C

Body composition and weight changes after ivacaftor treatment in adults with cystic fibrosis carrying the G551 D cystic fibrosis transmembrane conductance regulator mutation: A double-blind, placebo-controlled, randomized, crossover study with open-label extension.

primary studies  published RCT

Details
  • 2021
  • King SJ

Effects of a Short-Term Resistance-Training Program on Heart Rate Variability in Children With Cystic Fibrosis-A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2021
  • Estévez-González AJ

The clinical effects of combining postural exercises with chest physiotherapy in cystic fibrosis: A single-blind, randomized-controlled trial.

primary studies  published RCT

Details
  • 2021
  • Güngör S