CFDB - Cystic Fibrosis DataBase

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Safety and tolerability of denufosol tetrasodium inhalation solution, a novel P2Y2 receptor agonist: results of a phase 1/phase 2 multicenter study in mild to moderate cystic fibrosis.

primary studies  published RCT

Details
  • 2005
  • Deterding R

Inhaled beta-agonists improve lung function but not maximal exercise capacity in cystic fibrosis.

primary studies  published RCT

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  • 2005
  • Dodd JD

Evidence on improved outcomes with early diagnosis of cystic fibrosis through neonatal screening: enough is enough!.

primary studies  published RCT

Details
  • 2005
  • Farrell PM

A crossover, randomized, controlled trial of dornase alfa before versus after physiotherapy in cystic fibrosis.

primary studies  published RCT

Details
  • 2005
  • Fitzgerald DA

Short-term protein intake and stimulation of protein synthesis in stunted children with cystic fibrosis.

primary studies  published RCT

Details
  • 2005
  • Geukers VG

Oral L-arginine supplementation in cystic fibrosis patients: a placebo-controlled study.

primary studies  published RCT

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  • 2005
  • Grasemann H

Sequential analysis of surfactant, lung function and inflammation in cystic fibrosis patients.

primary studies  published RCT

Details
  • 2005
  • Griese M

Growth hormone treatment enhances nutrition and growth in children with cystic fibrosis receiving enteral nutrition.

primary studies  published RCT

Details
  • 2005
  • Hardin DS

Long-term trial of cyproheptadine as an appetite stimulant in cystic fibrosis.

primary studies  published RCT

Details
  • 2005
  • Homnick DN

Failure of conventional strategies to improve nutritional status in malnourished adolescents and adults with cystic fibrosis.

primary studies  published RCT

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  • 2005
  • Kalnins D