CFDB - Cystic Fibrosis DataBase

All subcategories » published, non RCT

Non-invasive evaluation of steatosis and fibrosis in the liver in adults patients living with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2025
  • Piñar-Gutiérrez A

Long-term impact of Elexacaftor/Tezacaftor/ivacaftor on pulmonary, nutritional and metabolic outcomes in homozygous F508del cystic fibrosis patients: A real-world cohort study.

primary studies  published, non RCT

Details
  • 2026
  • Perrotta N

Impact of elexacaftor/tezacaftor/ivacaftor on gastrointestinal outcomes, inflammation, exocrine pancreatic function and fat malabsorption: Report of PROMISE pediatric substudy.

primary studies  published, non RCT

Details
  • 2026
  • Green N

Advancing Cystic Fibrosis-Related Diabetes Care With Automated Insulin Delivery Systems.

primary studies  published, non RCT

Details
  • 2026
  • Grancini V

Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.

primary studies  published, non RCT

Details
  • 2026
  • Colin L

Real-World Impact of Elexacaftor/Tezacaftor/Ivacaftor on Health-Related Quality of Life in Adults with Cystic Fibrosis: A 12-Month Multicenter Cohort Study.

primary studies  published, non RCT

Details
  • 2026
  • Kharraz R

Effect of elexacaftor-tezacaftor-ivacaftor on bronchial dilatations in adolescents with cystic fibrosis: a multicentre prospective observational study.

primary studies  published, non RCT

Details
  • 2026
  • Sermet-Gaudelus I

Evaluating Long-Term Effectiveness of Cystic Fibrosis Modulator Therapies After Rapid Adoption: A Dual-Approach Study.

primary studies  published, non RCT

Details
  • 2025
  • Afonso PM

20 years of the Montreal Cystic Fibrosis Related Diabetes Screening Cohort: key insights.

primary studies  published, non RCT

Details
  • 2025
  • Alexandre-Heymann L

Respiratory Outcomes and Aspergillus Serology Following Elexacaftor/Tezacaftor/Ivacaftor Therapy in People with Cystic Fibrosis and a History of Aspergillus fumigatus Infection.

primary studies  published, non RCT

Details
  • 2025
  • Lanfranchi C