CFDB - Cystic Fibrosis DataBase

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Efficacy of Adding Oral N acetyl Cysteine Supplement to the Cystic Fibrosis Treatment Regimen: A Randomized Quasi-Experimental Trial.

primary studies  published RCT

Details
  • 2025
  • Keshavarz S

Long-Term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Adults and Adolescents with Cystic Fibrosis and at Least One F508del Allele: A Phase 3, Open-Label Extension Study.

primary studies  published RCT

Details
  • 2025
  • Daines CL

Cannabinoid receptor 2 agonist, lenabasum, for the treatment of pulmonary exacerbations in cystic fibrosis.

primary studies  published RCT

Details
  • 2025
  • West NE

MetaNeb Versus Usual Care During Exacerbations of Cystic Fibrosis: An RCT.

primary studies  published RCT

Details
  • 2025
  • Chapman N

Randomized Cross-Over Analysis of the Influence of Nitrogen Multiple Breath Washout on Spirometry in Monitoring Lung Function in Patients With Cystic Fibrosis and Primary Ciliary Dyskinesia.

primary studies  published RCT

Details
  • 2025
  • Schoop AC

Cystic Fibrosis Microbiome-directed Antibiotic Therapy Trial in Exacerbations Results Stratified (CFMATTERS): Results of a multi-centre randomised controlled trial.

primary studies  published RCT

Details
  • 2025
  • Plant BJ

The impact of probiotics on pulmonary, gastrointestinal, and growth outcomes in pediatric cystic fibrosis: a randomized controlled trial.

primary studies  published RCT

Details
  • 2025
  • Rahmani P

Insulin for early glycaemic abnormality in children with cystic fibrosis without cystic fibrosis-related diabetes (CF-IDEA): a randomised controlled trial.

primary studies  published RCT

Details
  • 2025
  • Hameed S

Elexacaftor/tezacaftor/ivacaftor in children aged ≥6 years with cystic fibrosis heterozygous for F508del and a minimal function mutation: Results from a 96-week open-label extension study.

primary studies  published RCT

Details
  • 2025
  • Mall MA

The Effects of Progressive Muscle Relaxation on Mental Health and Sleep Quality in Adults with Cystic Fibrosis: A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2025
  • Maritescu A