CFDB - Cystic Fibrosis DataBase

All subcategories » published RCT

Empire-CF study: A phase 2 clinical trial of leukotriene A4 hydrolase inhibitor acebilustat in adult subjects with cystic fibrosis.

primary studies  published RCT

Details
  • 2021
  • Elborn JS

Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations.

primary studies  published RCT

Details
  • 2020
  • Munck A

Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study.

primary studies  published RCT

Details
  • 2020
  • Nick JA

The benefits of mechanical insufflator-exsufflator compared to autogenic drainage in adults with cystic fibrosis.

primary studies  published RCT

Details
  • 2020
  • Helper N

Oral cysteamine as an adjunct treatment in cystic fibrosis pulmonary exacerbations: An exploratory randomized clinical trial.

primary studies  published RCT

Details
  • 2020
  • Devereux G

A phase 3, randomized, double-blind, parallel-group study to evaluate tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for F508del-CFTR and a gating mutation.

primary studies  published RCT

Details
  • 2020
  • McKone EF

Role of Tris-CaEDTA as an adjuvant with nebulised tobramycin in cystic fibrosis patients with Pseudomonas aeruginosa lung infections: A randomised controlled trial.

primary studies  published RCT

Details
  • 2020
  • Puvvadi R

The effectiveness of a mobile high-frequency chest wall oscillation (HFCWO) device for airway clearance.

primary studies  published RCT

Details
  • 2020
  • Leemans G

Long-term azithromycin use is not associated with QT prolongation in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2020
  • Magaret AS

Oral Glutathione and Growth in Cystic Fibrosis: A Multi-Center, Randomized, Placebo-Controlled, Double-Blind Trial.

primary studies  published RCT

Details
  • 2020
  • Bozic M