Empire-CF study: A phase 2 clinical trial of leukotriene A4 hydrolase inhibitor acebilustat in adult subjects with cystic fibrosis.
primary studies published RCT
Details- 2021
- Elborn JS
Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations.
primary studies published RCT
Details- 2020
- Munck A
Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study.
primary studies published RCT
Details- 2020
- Nick JA
The benefits of mechanical insufflator-exsufflator compared to autogenic drainage in adults with cystic fibrosis.
primary studies published RCT
Details- 2020
- Helper N
Oral cysteamine as an adjunct treatment in cystic fibrosis pulmonary exacerbations: An exploratory randomized clinical trial.
primary studies published RCT
Details- 2020
- Devereux G
A phase 3, randomized, double-blind, parallel-group study to evaluate tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for F508del-CFTR and a gating mutation.
primary studies published RCT
Details- 2020
- McKone EF
Role of Tris-CaEDTA as an adjuvant with nebulised tobramycin in cystic fibrosis patients with Pseudomonas aeruginosa lung infections: A randomised controlled trial.
primary studies published RCT
Details- 2020
- Puvvadi R
The effectiveness of a mobile high-frequency chest wall oscillation (HFCWO) device for airway clearance.
primary studies published RCT
Details- 2020
- Leemans G
Long-term azithromycin use is not associated with QT prolongation in children with cystic fibrosis.
primary studies published RCT
Details- 2020
- Magaret AS
Oral Glutathione and Growth in Cystic Fibrosis: A Multi-Center, Randomized, Placebo-Controlled, Double-Blind Trial.
primary studies published RCT
Details- 2020
- Bozic M