CFDB - Cystic Fibrosis DataBase

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Body composition and weight changes after ivacaftor treatment in adults with cystic fibrosis carrying the G551 D cystic fibrosis transmembrane conductance regulator mutation: A double-blind, placebo-controlled, randomized, crossover study with open-label extension.

primary studies  published RCT

Details
  • 2021
  • King SJ

Effects of a Short-Term Resistance-Training Program on Heart Rate Variability in Children With Cystic Fibrosis-A Randomized Controlled Trial.

primary studies  published RCT

Details
  • 2021
  • Estévez-González AJ

The clinical effects of combining postural exercises with chest physiotherapy in cystic fibrosis: A single-blind, randomized-controlled trial.

primary studies  published RCT

Details
  • 2021
  • Güngör S

Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial.

primary studies  published RCT

Details
  • 2021
  • Spoletini G

Association of Intensity of Anti-Pseudomonal Antibiotic Therapy With Risk of Treatment-Emergent Organisms in Cystic Fibrosis Children with Newly Acquired Pseudomonas Aeruginosa.

primary studies  published RCT

Details
  • 2021
  • Cogen JD

Efficacy and safety of inhaled dry-powder mannitol in adults with cystic fibrosis: An international, randomized controlled study.

primary studies  published RCT

Details
  • 2021
  • Flume PA

Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial.

primary studies  published RCT

Details
  • 2021
  • Griese M

Reflex zone stimulation reduces ventilation inhomogeneity in cystic fibrosis: A randomised controlled cross-over study.

primary studies  published RCT

Details
  • 2021
  • Jana P

Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2021
  • Voldby C

How Many Maneuvers Should We Do for Maximal Inspiratory and Expiratory Muscle Pressure Testing in Children: A Retrospective Review in Children with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2021
  • Boonjindasup W