CFDB - Cystic Fibrosis DataBase

Evaluation of the safety of amantadine-HCl and the role of respiratory viral infections in children with cystic fibrosis.

primary studies  published RCT

Details
  • 1976
  • Wright PF

Influence of mist tent therapy on sputum viscosity and water content in cystic fibrosis.

primary studies  published RCT

Details
  • 1974
  • Rosenbluth M

Assessment of medium-chain triglyceride feeding in infants with cystic fibrosis.

primary studies  published RCT

Details
  • 1969
  • Gracey M

A double-blind study of the use of acetylcysteine in patients with cystic fibrosis.

primary studies  published RCT

Details
  • 1966
  • Howatt WF

Studies of tocopherol deficiency in infants and children: VI. Evaluation of muscle strength and effect of tocopherol administration in children with cystic fibrosis.

primary studies  published RCT

Details
  • 1961
  • Levin S

Non-invasive evaluation of steatosis and fibrosis in the liver in adults patients living with cystic fibrosis.

primary studies  published, non RCT

Details
  • 2025
  • Piñar-Gutiérrez A

Long-term impact of Elexacaftor/Tezacaftor/ivacaftor on pulmonary, nutritional and metabolic outcomes in homozygous F508del cystic fibrosis patients: A real-world cohort study.

primary studies  published, non RCT

Details
  • 2026
  • Perrotta N

Impact of elexacaftor/tezacaftor/ivacaftor on gastrointestinal outcomes, inflammation, exocrine pancreatic function and fat malabsorption: Report of PROMISE pediatric substudy.

primary studies  published, non RCT

Details
  • 2026
  • Green N

Advancing Cystic Fibrosis-Related Diabetes Care With Automated Insulin Delivery Systems.

primary studies  published, non RCT

Details
  • 2026
  • Grancini V

Persistence of lung hyperinflation and small airway dysfunction in school-aged children with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: results from the real-world MODUL-CF study.

primary studies  published, non RCT

Details
  • 2026
  • Colin L