CFDB - Cystic Fibrosis DataBase

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Respiratory muscle training improves respiratory muscle endurance but not exercise tolerance in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2017
  • Bieli C

Lack of efficacy of Lactobacillus GG in reducing pulmonary exacerbations and hospital admissions in children with cystic fibrosis: A randomised placebo controlled trial.

primary studies  published RCT

Details
  • 2017
  • Bruzzese E

Inhaled dry powder mannitol in children with cystic fibrosis: A randomised efficacy and safety trial.

primary studies  published RCT

Details
  • 2017
  • De Boeck K

Effect of synbiotic supplementation in children and adolescents with cystic fibrosis: a randomized controlled clinical trial.

primary studies  published RCT

Details
  • 2017
  • de Freitas MB

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.

primary studies  published RCT

Details
  • 2017
  • Donaldson SH

Effects of treadmill exercise versus Flutter(R) on respiratory flow and sputum properties in adults with cystic fibrosis: a randomised, controlled, cross-over trial.

primary studies  published RCT

Details
  • 2017
  • Dwyer TJ

Ease of use of tobramycin inhalation powder compared with nebulized tobramycin and colistimethate sodium: a crossover study in cystic fibrosis patients with pulmonary Pseudomonas aeruginosa infection

primary studies  published RCT

Details
  • 2017
  • Greenwood J

Chest physiotherapy can affect the lung clearance index in cystic fibrosis patients.

primary studies  published RCT

Details
  • 2017
  • Grosse-Onnebrink J

Bolus weekly vitamin D3 supplementation impacts gut and airway microbiota in adults with cystic fibrosis: a double-blind, randomized, placebo-controlled clinical trial.

primary studies  published RCT

Details
  • 2017
  • Kanhere M

Improvement in exercise duration, lung function and well-being in G551D-Cystic Fibrosis patients: a double-blind, placebo-controlled, randomised, cross-over study with ivacaftor.

primary studies  published RCT

Details
  • 2017
  • Keating DT