CFDB - Cystic Fibrosis DataBase

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Home Monitoring of Patients with Cystic Fibrosis to Identify and Treat Acute Pulmonary Exacerbations. eICE Study Results.

primary studies  published RCT

Details
  • 2017
  • Lechtzin N

In vivo and in vitro ivacaftor response in cystic fibrosis patients with residual CFTR function: N-of-1 studies.

primary studies  published RCT

Details
  • 2017
  • McGarry ME

Physical Activity Counseling for Children With Cystic Fibrosis.

primary studies  published RCT

Details
  • 2017
  • Moola FJ

Microbiological efficacy of early MRSA treatment in cystic fibrosis in a randomised controlled trial.

primary studies  published RCT

Details
  • 2017
  • Muhlebach MS

Effects of inhaled hypertonic (7%) saline on lung function test in preschool children with cystic fibrosis: results of a crossover, randomized clinical trial.

primary studies  published RCT

Details
  • 2017
  • Nenna R

Efficacy and safety of lumacaftor and ivacaftor in patients aged 6-11 years with cystic fibrosis homozygous for F508del-CFTR: a randomised, placebo-controlled phase 3 trial.

primary studies  published RCT

Details
  • 2017
  • Ratjen F

Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2017
  • Rowe SM

Lumacaftor/Ivacaftor Treatment of Patients with Cystic Fibrosis Heterozygous for F508del-CFTR.

primary studies  published RCT

Details
  • 2017
  • Rowe SM

Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del.

primary studies  published RCT

Details
  • 2017
  • Taylor-Cousar JL

Long-Term Pulmonal Therapy of Cystic Fibrosis-Patients with Amitriptyline.

primary studies  published RCT

Details
  • 2016
  • Adams C