CFDB - Cystic Fibrosis DataBase

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Bolus weekly vitamin D3 supplementation impacts gut and airway microbiota in adults with cystic fibrosis: a double-blind, randomized, placebo-controlled clinical trial.

primary studies  published RCT

Details
  • 2017
  • Kanhere M

Improvement in exercise duration, lung function and well-being in G551D-Cystic Fibrosis patients: a double-blind, placebo-controlled, randomised, cross-over study with ivacaftor.

primary studies  published RCT

Details
  • 2017
  • Keating DT

Home Monitoring of Patients with Cystic Fibrosis to Identify and Treat Acute Pulmonary Exacerbations. eICE Study Results.

primary studies  published RCT

Details
  • 2017
  • Lechtzin N

In vivo and in vitro ivacaftor response in cystic fibrosis patients with residual CFTR function: N-of-1 studies.

primary studies  published RCT

Details
  • 2017
  • McGarry ME

Physical Activity Counseling for Children With Cystic Fibrosis.

primary studies  published RCT

Details
  • 2017
  • Moola FJ

Microbiological efficacy of early MRSA treatment in cystic fibrosis in a randomised controlled trial.

primary studies  published RCT

Details
  • 2017
  • Muhlebach MS

Effects of inhaled hypertonic (7%) saline on lung function test in preschool children with cystic fibrosis: results of a crossover, randomized clinical trial.

primary studies  published RCT

Details
  • 2017
  • Nenna R

Efficacy and safety of lumacaftor and ivacaftor in patients aged 6-11 years with cystic fibrosis homozygous for F508del-CFTR: a randomised, placebo-controlled phase 3 trial.

primary studies  published RCT

Details
  • 2017
  • Ratjen F

Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis.

primary studies  published RCT

Details
  • 2017
  • Rowe SM

Lumacaftor/Ivacaftor Treatment of Patients with Cystic Fibrosis Heterozygous for F508del-CFTR.

primary studies  published RCT

Details
  • 2017
  • Rowe SM