A randomized controlled trial to evaluate the lung clearance index as an outcome measure for early phase studies in patients with cystic fibrosis.
primary studies published RCT
Details- 2016
- Amin R
Nutritional Status Improved in Cystic Fibrosis Patients with the G551D Mutation After Treatment with Ivacaftor.
primary studies published RCT
Details- 2016
- Borowitz D
Pilot Randomized Controlled Trial Evaluating the Effect of Hypertonic Saline With and Without Hyaluronic Acid in Reducing Inflammation in Cystic Fibrosis.
primary studies published RCT
Details- 2016
- Brivio A
Infant lung function tests as endpoints in the ISIS multicenter clinical trial in cystic fibrosis.
primary studies published RCT
Details- 2016
- Davis SD
A randomised trial of hypertonic saline during hospitalisation for exacerbation of cystic fibrosis.
primary studies published RCT
Details- 2016
- Dentice RL
Efficacy and safety of lumacaftor/ivacaftor combination therapy in patients with cystic fibrosis homozygous for Phe508del CFTR by pulmonary function subgroup: a pooled analysis.
primary studies published RCT
Details- 2016
- Elborn JS
A phase 3, multi-center, multinational, randomized, double-blind, placebo-controlled study to evaluate the efficacy and safety of levofloxacin inhalation solution (APT-1026) in stable cystic fibrosis patients.
primary studies published RCT
Details- 2016
- Flume PA
Continuous alternating inhaled antibiotics for chronic pseudomonal infection in cystic fibrosis.
primary studies published RCT
Details- 2016
- Flume PA
Inhaled alpha1-proteinase inhibitor therapy in patients with cystic fibrosis.
primary studies published RCT
Details- 2016
- Gaggar A
A Prospective, Randomized, Double-Blind, Parallel-Group, Comparative Effectiveness Clinical Trial Comparing a Powder Vehicle Compound of Vitamin D With an Oil Vehicle Compound in Adults With Cystic Fibrosis.
primary studies published RCT
Details- 2016
- Hermes WA