CFDB - Cystic Fibrosis DataBase

Pilot safety study of liposomal prostaglandin (PGE1) in respiratory exacerbations in cystic fibrosis.

primary studies  published RCT

Details
  • 2002
  • Taylor CJ

A phase II, double-blind, randomized, placebo-controlled clinical trial of tgAAVCF using maxillary sinus delivery in patients with cystic fibrosis with antrostomies.

primary studies  published RCT

Details
  • 2002
  • Wagner JA

Once-daily tobramycin in the treatment of adult patients with cystic fibrosis.

primary studies  published RCT

Details
  • 2002
  • Whitehead A

Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: a randomised trial.

primary studies  published RCT

Details
  • 2002
  • Wolter J

Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate.

primary studies  published RCT

Details
  • 2002
  • Zeitlin PL

Effect of insulinlike growth factor-1 treatment in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Bucuvalas JC

Cystic fibrosis-related deaths in infancy and the effect of newborn screening.

primary studies  published RCT

Details
  • 2001
  • Doull IJ

RAD in stable lung and heart/lung transplant recipients: safety, tolerability, pharmacokinetics, and impact of cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Doyle RL

Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group.

primary studies  published RCT

Details
  • 2001
  • Farrell PM

In vivo physiologic comparison of two ventilators used for domiciliary ventilation in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Fauroux B