CFDB - Cystic Fibrosis DataBase

RAD in stable lung and heart/lung transplant recipients: safety, tolerability, pharmacokinetics, and impact of cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Doyle RL

Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group.

primary studies  published RCT

Details
  • 2001
  • Farrell PM

In vivo physiologic comparison of two ventilators used for domiciliary ventilation in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Fauroux B

Growth hormone improves clinical status in prepubertal children with cystic fibrosis: results of a randomized controlled trial.

primary studies  published RCT

Details
  • 2001
  • Hardin DS

Growth hormone decreases protein catabolism in children with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Hardin DS

Effect of intravenous pamidronate on bone mineral density in adults with cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • Haworth CS

Glucocorticoid treatment reduces exhaled nitric oxide in cystic fibrosis patients.

primary studies  published RCT

Details
  • 2001
  • Linnane SJ

Microbiological and immunologic considerations with aerosolized drug delivery.

primary studies  published RCT

Details
  • 2001
  • LiPuma JJ

Efficacy of once-daily tobramycin monotherapy for acute pulmonary exacerbations of cystic fibrosis: a preliminary study.

primary studies  published RCT

Details
  • 2001
  • Master V

Long-term comparative trial of positive expiratory pressure versus oscillating positive expiratory pressure (flutter) physiotherapy in the treatment of cystic fibrosis.

primary studies  published RCT

Details
  • 2001
  • McIlwaine PM